CLN8 Rabbit pAb (APR23389N)
產(chǎn)品名稱： CLN8 Rabbit pAb (APR23389N)
英文名稱： CLN8 Rabbit pAb (APR23389N)
產(chǎn)品編號(hào)： APR23389N
產(chǎn)品價(jià)格： null
產(chǎn)品產(chǎn)地： 美國
品牌商標(biāo)： Leading Biology
更新時(shí)間： null
使用范圍：
生物谷
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分子量：Observed MW: 33kDa 稀釋方法：WB 1:500 - 1:2000 IHC 1:50 - 1:300 總結(jié)：This gene encodes a transmembrane protein belonging to a family of proteins containing TLC domains, which are postulated to function in lipid synthesis, transport, or sensing. The protein localizes to the endoplasmic reticulum (ER), and may recycle between the ER and ER-Golgi intermediate compartment. Mutations in this gene are associated with progressive epilepsy with mental retardation (EMPR), which is a subtype of neuronal ceroid lipofuscinoses (NCL). Patients with mutations in this gene have altered levels of sphingolipid and phospholipids in the brain.