ACOX1 Rabbit pAb (APR27950N)-抗體-抗體-生物在線
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ACOX1 Rabbit pAb (APR27950N)

ACOX1 Rabbit pAb (APR27950N)

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產品名稱: ACOX1 Rabbit pAb (APR27950N)

英文名稱: ACOX1 Rabbit pAb (APR27950N)

產品編號: APR27950N

產品價格: null

產品產地: 美國

品牌商標: Leading Biology

更新時間: null

使用范圍: WB (Mus musculus, Sus scrofa, Rattus norvegicus, Homo sapiens)

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分子量:Calculated MW: 70kDa/74kDa
Observed MW: 74KDa/50KDa

細胞定位:Peroxisome

稀釋方法:WB 1:500 - 1:2000
IHC 1:100 - 1:200
IF 1:50 - 1:200

總結:The protein encoded by this gene is the first enzyme of the fatty acid beta-oxidation pathway, which catalyzes the desaturation of acyl-CoAs to 2-trans-enoyl-CoAs. It donates electrons directly to molecular oxygen, thereby producing hydrogen peroxide. Defects in this gene result in pseudoneonatal adrenoleukodystrophy, a disease that is characterized by accumulation of very long chain fatty acids. Alternatively spliced transcript variants encoding different isoforms have been identified.