ABAT肽
產(chǎn)品名稱： ABAT肽
英文名稱： S) 3 amino 2 methylpropionate transaminase (S)-3-amino-2-methylpropionate transaminase 4 aminobutyrate aminotransferase 4 aminobutyrate amin
產(chǎn)品編號(hào)： ab202287
產(chǎn)品價(jià)格： 0
產(chǎn)品產(chǎn)地： 英國(guó)
品牌商標(biāo)： abcam
更新時(shí)間： null
使用范圍： null
深圳市宇德立生物科技有限公司
- 聯(lián)系人 :
- 地址 : 深圳市寶安區(qū)西鄉(xiāng)寶民二路賢基大廈4E
- 郵編 :
- 所在區(qū)域 : 廣東
- 電話 : 133****4454 點(diǎn)擊查看
- 傳真 : 點(diǎn)擊查看
- 郵箱 : 1484332550@qq.com
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- 應(yīng)用
Blocking - Blocking peptide for Anti-ABAT antibody [EPR4433] (ab108249)
- 形式Liquid
- 補(bǔ)充說(shuō)明
This is the blocking peptide for?ab108249
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濃度100 μg 濃度為 1 mg/ml?
制備和貯存
- 穩(wěn)定性和存儲(chǔ)
Shipped at 4°C. Store at -20°C.
常規(guī)信息
-
別名
- (S) 3 amino 2 methylpropionate transaminase
- (S)-3-amino-2-methylpropionate transaminase
- 4 aminobutyrate aminotransferase
- 4 aminobutyrate aminotransferase, mitochondrial
- 4-aminobutyrate aminotransferase
- ABAT
- FLJ17813
- FLJ30272
- GABA aminotransferase
- GABA AT
- GABA T
- GABA transaminase
- GABA transferase
- GABA-AT
- GABA-T
- GABAT
- GABT_HUMAN
- Gamma amino N butyrate transaminase
- Gamma-amino-N-butyrate transaminase
- hCG1984265
- L AIBAT
- L-AIBAT
- LAIBAT
- mitochondrial
- NPD009
hide - 功能Catalyzes the conversion of gamma-aminobutyrate and L-beta-aminoisobutyrate to succinate semialdehyde and methylmalonate semialdehyde, respectively. Can also convert delta-aminovalerate and beta-alanine.
- 組織特異性Liver > pancreas > brain > kidney > heart > placenta.
- 疾病相關(guān)Defects in ABAT are a cause of gamma-aminobutyrate transaminase deficiency (GABA-AT deficiency) [MIM:613163]. The phenotype of this deficiency includes psychomotor retardation, hypotonia, hyperreflexia, lethargy, refractory seizures, and EEG abnormalities.
- 序列相似性Belongs to the class-III pyridoxal-phosphate-dependent aminotransferase family.
- 細(xì)胞定位Mitochondrion matrix.